A Congenital Deadly Association: Dilated Cardiomyopathy and Long QT Syndrome


  • Neiberg de Alcantara Lima Western Michigan University – Homer Stryker M.D. School of Medicine – Department of Internal Medicine – Kalamazoo/MI – USA.
  • Antonio Thomaz de Andrade Hospital de Messejana – Fortaleza/CE – Brazil.
  • Stela M V Sampaio Hospital de Messejana – Fortaleza/CE – Brazil.
  • Mark Loehrke Western Michigan University Homer Stryker – School of Medicine – Internal Medicine – Kalamazoo (MI), USA.


Long QT Syndrome, Cardiomyopathies, Genetic Diseases, Ventricular Tachycardia, Channelopathies


Long QT syndrome is one of the most feared entities in hospitalized patients due to the potential risk for ventricular tachycardia and sudden death. Association between channelopathies and congenital cardiomyopathy is a new entity that has been studied recently. We report an interesting case of this association that maybe related to a genetic mutation.


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How to Cite

Lima, N. de A., Andrade, A. T. de ., Sampaio, S. M. V. ., & Loehrke, M. (2020). A Congenital Deadly Association: Dilated Cardiomyopathy and Long QT Syndrome. JOURNAL OF CARDIAC ARRHYTHMIAS, 33(4). Retrieved from https://www.jca.org.br/jca/article/view/3426



Clinical Arrythmia