Sick sinus syndrome in young woman with Mayer-Rokitansky-Küster-Hauser syndrome

Coincidence or associated comorbidity?


  • Marcel Pereira Moussa
  • André Soares Maria
  • Cristiano de Oliveira Dietrich
  • Luciana Vidal Armaganijan


Vagina/Abnormalities, Sick Sinus Syndrome, Congenital Abnormalities


Case report of a 39-year-old woman with Mayer-Rokitansky-Küster-Hauser syndrome and sick sinus syndrome requiring a definitive pacemaker. As a young patient, without secondary causes of bradycardia, we suggest the possibility of a relationship between these two diseases, since there are reports of the association of Mayer-Rokitansky-Küster-Hauser syndrome and structural heart diseases, and no reports of a relationship with bradycardia until now.


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How to Cite

Pereira Moussa, M., Soares Maria, A., de Oliveira Dietrich, C., & Vidal Armaganijan, L. (2017). Sick sinus syndrome in young woman with Mayer-Rokitansky-Küster-Hauser syndrome: Coincidence or associated comorbidity?. JOURNAL OF CARDIAC ARRHYTHMIAS, 31(3), 89–91. Retrieved from



Clinical Arrythmia